Living TODAY With Primary Pulmonary Hypertension (PPH)

My sister, Quillarene Baker Rice, nicknamed Renie,and nephews with encouragement for their continued
died at the age of forty-five due to the progressioneducational success.
of a terminal respiratory disease. She was anLife was too valuable to her to waste with self-pity
attractive, vibrant and upbeat young womanand depressive spells. It was her faith in GOD that
seemingly with her entire life ahead of her. Little didhelped her during lonely times when she was confined
she know that on July 15, 1998, doctors wouldat home. Scripture promises in the Book of Psalms
diagnose her breathlessness and fatigue as Primaryand gospel music were tools she used to buoy her
Pulmonary Hypertension, (PPH) and prescribedspirits.
twenty-four hour oxygen therapy. Very littleShe often quoted, "Yea, though I walk through the
knowledge about PPH was available at that time. It isvalley of the shadow of death, I will fear no evil; for
so rare and without a known cause, that statisticallyYou are with me; Your rod and Your staff, they
it occurs in about two persons per million each year.comfort me. (Psalm 23:4, KJV)
However, the symptoms, shortness of breath withDiagnosed each year in the United States are an
minimal exertion, fatigue, chest pain, dizzy spells andestimated 500 to 1,000 new cases of PPH. Additional
fainting, results in PPH being frequently misdiagnosed.treatments have been developed and approved over
It often progresses to the late stages beforethe last six years since my sister's death. People are
discovery. The greatest numbers of PPH cases occurdoing so much better, living longer and enjoying a
in women from ages 20 to 40; however, men andhigher quality of life. Today there are more
children can also develop this disease. There is noopportunities for those with a PPH diagnosis to reach
known cure for PPH so the goal of treatment is toout to others. Supplementary information amassed
control symptoms.and disseminated through the National Organization of
Renie was not a candidate for a complete heart andRare Diseases (NORD), about healthy diet choices,
lung transplant that could have increased her lifestress reduction, rest, and relaxation tips are all
expectancy. Unfortunately, this procedure involvesstrategies made available for coping day to day with
another set of obstacles in obtaining a donor. HerPPH.
treatment involved large oxygen machines to use atToday numerous groups have formed for the
home and the portable type for excursions. AroundPulmonary Hypertension community to share info,
the clock oxygen therapy greatly diminished therelate personal experiences and seek prayer. There
quality of her life. Many everyday tasks such asare an increased number of books, publications and
bathing and preparing a meal left her gasping for herwebsites now from those managing all of the
next breath, if somehow the oxygen flow becamechallenges of this disease than were available during
blocked. Trips to the grocery store, cleaners andthe last years of my sister's life. Support groups like
even doctor visits were an ordeal if enough portablethe Pulmonary Hypertension Association have
oxygen was not anticipated. (Being stuck in trafficmobilized to raise funds for research via concerts,
could cause full-scale panic!)conferences, golf tournaments, walk-a-thons and
Initially, Renie worked from home a couple of days aother social events.
week. As the disease progressed, she reduced theNovember is Pulmonary Hypertension Awareness
number of days that she went into her office untilmonth. This year marks the ten-year anniversary of
gradually she worked from home full time. Doctora national initiative to create awareness for what
visits for my sister were numerous. Fortunately, sheonce was an obscure illness. Today millions of dollars
had the loving support of her mother, daughter, twinare committed to the search for a cure. Although
sister and other siblings to accompany her to theseRenie lived a little over three years after her
visits and other trips when needed. Even with thediagnosis, today there are cases of those living
deadly prognosis before her, Renie was determinedtwenty years and beyond. With the heightened
to enjoy her remaining time on earth. Her prayer wasinvolvement of the public to combat this disease,
to see her daughter graduate from high school andthere is hope and encouragement for those living
settle into college. Always with a positive and upbeatwith PPH today!
attitude, she made it her mission to call her nieces